Hereditary CD4+ T lymphocytopenia.

نویسندگان

  • S Freier
  • E Kerem
  • Z Dranitzki
  • M Schlesinger
  • R Rabinowitz
  • C Brautbar
  • M Ashkirat
  • Y Naparstek
چکیده

Two siblings suffering from mental retardation, progressive bronchiectasis, extensive warts, and persistent hepatitis B are described. The propositus also had an unusual physiognomy and non-specific colitis. Both patients had a marked decrease in the population of CD4+ helper T cells.

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عنوان ژورنال:
  • Archives of disease in childhood

دوره 78 4  شماره 

صفحات  -

تاریخ انتشار 1998